{"id":52,"date":"2015-05-08T18:37:21","date_gmt":"2015-05-08T18:37:21","guid":{"rendered":"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/?page_id=52"},"modified":"2015-05-08T18:49:36","modified_gmt":"2015-05-08T18:49:36","slug":"artigos-cientificos","status":"publish","type":"page","link":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/artigos-cientificos\/","title":{"rendered":"Artigos Cient\u00edficos"},"content":{"rendered":"<p>MPS EM GERAL<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/Farmacovigilancia-Reacoes-Adversas-a-Medicamentos-.pdf\">Farmacovigil\u00e2ncia: Rea\u00e7\u00f5es Adversas a Medicamentos<\/a> &#8211; Boletim informativo do CIM-RS (2008)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/mucopolysaccharidoses_in_brazil.pdf\">Mucopolysaccharidoses in Brazil: What Happens From Birth to Biochemical Diagnosis?<\/a> &#8211; American Journal of Medical Genetics (2008)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/Twelve_different_enzyme_assays_on_dried-blood_filter_paper_samples.pdf\">Twelve different enzyme assays on dried-blood filter paper samples for detection of patients with selected inherited lysosomal storage diseases<\/a> &#8211; Clinica Chimica Acta (2006)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/enzyme.pdf\">Enzyme Assays on Dried Blood Filter Paper Samples for Specific Detection of Selected Inherited Lysosomal Storage Diseases<\/a> &#8211; Current Medical Literature (2007)<\/p>\n<p>MPS I<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/CONSENSO.pdf\">Consenso de diagn\u00f3stico y tratamiento de la mucopolisacaridosis de tipo I<\/a> &#8211; Arch Argent Pediatr (2008)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/guidelines.pdf\">Guidelines for the Investigation and Management of Mucopolysaccharidosis type I<\/a> &#8211; Department of Health, UK (2008)<\/p>\n<p>MPS II<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/A-PHASE.pdf\">A phase II\/III clinical study of enzyme replacement therapy with idursulfase in mucopolysaccharidosis II (Hunter syndrome)<\/a> &#8211; Genetics IN Medicine (2006)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/PROSPECTIVE.pdf\">Prospective study of 11 Brazilian patients with mucopolysaccharidosis II <\/a>&#8211; Jornal de Pediatria (2006)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/AVALIACAO-PROSPECTIVA.pdf\">Avalia\u00e7\u00e3o prospectiva de 11 pacientes brasileiros com mucopolissacaridose II<\/a> &#8211; Jornal de Pediatria (2006)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/GUIDELINES.pdf\">Guidelines for the Investigation and Management of Mucopolysaccharidosis type II<\/a> &#8211; Department of Health, UK (2008)<\/p>\n<p>MPS VI<\/p>\n<p>ERT for MPS VI: A Phase 3, Randomized, Double-Blind, Placebo-Controlled, Multinational Study and Follow-on, Open Label Extension Study &#8211; Jornal de Pediatria (2006)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/thesgold.pdf\">Threshold Effect of Urinary Glycosaminoglycans and the Walk Test as indicator of Disease Progression in a Survey of Subjects With Mucopolysaccharidoses VI<\/a> &#8211; American Journal of Medical Genetics (2005)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/assessment.pdf\">Assessment of joint mobility and grip and pinch strength<\/a> &#8211; Jornal de Pediatria (2008)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/mucopoli.pdf\">Mucopolissacaridose tipo VI (s\u00edndrome de Maroteaux-Lamy): avalia\u00e7\u00e3o da mobilidade articular e das for\u00e7as de garra e de pin\u00e7a<\/a> &#8211; Jornal de Pediatria (2008)<\/p>\n<p>Management Guidelines for Mucopolysaccharidosis VI &#8211; Pediatrics (2007)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/guidelines1.pdf\">Guidelines for the Investigation and Management of Mucopolysaccharidosis type VI<\/a> &#8211; Department of Health, UK (2008)<\/p>\n<p><a href=\"http:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-content\/uploads\/sites\/2\/2015\/05\/aldes.pdf\">Alder-Reilly Anomaly in Patients With Mucopolysaccharidosis VI<\/a> &#8211; Rev HCPA (2008)<\/p>\n","protected":false},"excerpt":{"rendered":"<p>MPS EM GERAL Farmacovigil\u00e2ncia: Rea\u00e7\u00f5es Adversas a Medicamentos &#8211; Boletim informativo do CIM-RS (2008) Mucopolysaccharidoses in Brazil: What Happens From Birth to Biochemical Diagnosis? &#8211; American Journal of Medical Genetics (2008) Twelve different enzyme assays on dried-blood filter paper samples for detection of patients with selected inherited lysosomal storage diseases &#8211; Clinica Chimica Acta (2006) [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"open","ping_status":"open","template":"","meta":[],"_links":{"self":[{"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/pages\/52"}],"collection":[{"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/comments?post=52"}],"version-history":[{"count":5,"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/pages\/52\/revisions"}],"predecessor-version":[{"id":59,"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/pages\/52\/revisions\/59"}],"wp:attachment":[{"href":"https:\/\/www.ufrgs.br\/geneticahcpa\/rede-mps\/wp-json\/wp\/v2\/media?parent=52"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}